Anaesthetic management of vaginal delivery in a woman with Friedreich's ataxia complicated by cardiomyopathy and scoliosis.
نویسندگان
چکیده
We report the anaesthetic management of vaginal delivery in a woman with Friedreich's ataxia, who had hypertrophic cardiomyopathy and had previously undergone thoracic spinal fusion with Harrington rod fixation. Combined spinal-epidural analgesia was used. Options for the anaesthetic management of labour and delivery are discussed.
منابع مشابه
Anaesthesia for a patient with Friedreich's ataxia and cardiomyopathy.
Friedreich's ataxia is an inherited neuromuscular disorder often associated with significant cardiac disease. We report a case of Friedreich's ataxia in a 13-year-old girl with ulcerative colitis and hypertrophic cardiomyopathy who was successfully managed for subtotal colectomy with general anaesthesia and epidural narcotic. Anaesthetic considerations included the maintenance of fluid volume a...
متن کاملFriedreich's ataxia cardiomyopathy: case based discussion and management issues.
Cardiac involvement is common in Friedreich's Ataxia and is a common cause of premature death. Evidence regarding treatment of congestive heart failure in patients with Friedreich's Ataxia is lacking. The case of a 31-year-old male with advanced Friedreich's Ataxia who presented with an acute diarrhoeal illness and features of acute heart failure is discussed. We then review the reported cardia...
متن کاملFriedreich's ataxia 1980. An overview of the physiopathology.
Phase three of the Quebec Cooperative Study of Friedreich's Ataxia was devoted to an understanding of the physiopathology of individual symptoms on the basis of previously discovered biochemical leads. The present paper attempts to pull these results together by presenting, as a hypothesis, a unifying scheme of possible interactions and relationships. The central core of this hypothesis is the ...
متن کاملLarge left ventricular thrombus in a patient with Friedreich's ataxia.
analysis of the courses of 43 patients with univentricular heart palliated by pulmonary artery banding. Deanfield JE. Is banding of the pulmonary trunk obsolete for infants with tricuspid atresia and double inlet ventri-cle with a discordant ventriculo-arterial connection? Role of aortic arch obstruction and subaortic stenosis. 7 Am Use of inhaled nitric oxide and acetylcholine in the evaluatio...
متن کاملNovel Missense Mitochondrial ND4L Gene Mutations in Friedreich's Ataxia
Objective(s) The mitochondrial defects in Friedreich's ataxia have been reported in many researches. Mitochondrial DNA is one of the candidates for defects in mitochondrion, and complex I is the first and one of the largest catalytic complexes of oxidative phosphorylation (OXPHOS) system. Materials and Methods We searched the mitochondrial ND4L gene for mutations by TTGE and sequencing on 30...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
عنوان ژورنال:
- International journal of obstetric anesthesia
دوره 7 3 شماره
صفحات -
تاریخ انتشار 1998